factor xiii deficiency, review of the literature and report of a case

نویسندگان

mojtaba vahid golpayegani department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran

hossein behnia department of oral & maxillofacial surgery, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

mahvareh akhgar araghi pedodontist, tehran, ir iranسازمان اصلی تایید شده: دانشگاه علوم پزشکی شهید بهشتی (shahid beheshti university of medical sciences)

ghassem ansari department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran; department of pediatric dentistry, school of dentistry, shahid beheshti university of medical sciences, tehran, ir iran. tel: +98-21 22255537

چکیده

conclusions the case was fully investigated and diagnosed as a case with factor xiii deficiency causing such uncontrolled bleeding after extraction of a tooth. introduction factor xiii deficiency is a relatively rare hereditary bleeding disorder, which is usually found during infancy or early childhood. this condition may involve both genders within different races in an equal manner. its incidence is estimated at approximately 1 in 106 live births. patients with factor xiii deficiency are presented with a pattern of neonatal hemorrhage and lifelong bleeding diathesis. case presentation a five-year-old female is presented here, who was diagnosed as a definite case of factor xiii deficiency, based on the clinical and laboratory findings at a medical specialist clinic. typical clinical features of the disorder were the chief complaint of the patient, which was severe bleeding when she was brought into a specialized dental office following an earlier dental procedure.

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عنوان ژورنال:
journal of comprehensive pediatrics

جلد ۷، شماره ۴، صفحات ۰-۰

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